Emir
FAMILIAL ATRIAL SEPTAL DEFECT
patches in both patients. They had uneventful postoperative genealogical tree of this family suggested autosomal
courses and were discharged on the 5th postoperative dominant transmission of the condition. We believe that
day. There were no dysrhythmias during the postoperative definition of inheritance of congenital heart disease in a
hospital stay.
specific family has important consequences and in a patient
with ASD, the presence of atrioventricular conduction
abnormalities should prompt a detailed family history.
DISCUSSION
Hereditary ASD is a rare lesion, generally transmitted in
an autosomal dominant fashion, which may show highly
variable phenotypic and genotypic features. Familial
forms of ASD are characterized by a high incidence of
associated cardiac and noncardiac lesions such as
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ASIAN CARDIOVASCULAR & THORACIC ANNALS